Roberta Besio

In utero transplantation of adult bone marrow decreases perinatal lethality and rescues the bone phenotype in the knockin murine model for classical, dominant osteogenesis imperfecta

Cristina Panaroni, Roberta Gioia, Anna Lupi et al. · Blood · 2009 · 108 citations

Medicine, Developmental Biology, Genetics +13

4-PBA ameliorates cellular homeostasis in fibroblasts from osteogenesis imperfecta patients by enhancing autophagy and stimulating protein secretion

Roberta Besio, Giusy Iula, Nadia Garibaldi et al. · Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease · 2018 · 91 citations · Full text

Life Sciences, Cell Biology, Molecular Medicine +17

Severely Impaired Bone Material Quality in Chihuahua Zebrafish Resembles Classical Dominant Human Osteogenesis Imperfecta

Imke A.K. Fiedler, Felix N. Schmidt, Eva Maria Wölfel et al. · Journal of Bone and Mineral Research · 2018 · 80 citations · Full text

Medicine, Animal Sciences, Animal Anatomy +16

Impaired Osteoblastogenesis in a Murine Model of Dominant Osteogenesis Imperfecta: A New Target for Osteogenesis Imperfecta Pharmacological Therapy

Roberta Gioia, Cristina Panaroni, Roberta Besio et al. · Stem Cells · 2012 · 79 citations · Full text

Medicine, Cell Biology, Genetics +17

Cellular stress due to impairment of collagen prolyl hydroxylation complex is rescued by the chaperone 4-phenylbutyrate

Roberta Besio, Nadia Garibaldi, Laura Leoni et al. · Disease Models & Mechanisms · 2019 · 62 citations · Full text

Life Sciences, Biochemistry, Cell Biology +17