Type I and Ir pleuropulmonary blastoma (PPB): A report from the International PPB/<i>DICER1</i> Registry

Abstract

For young children with type I PPB, outcomes are favorable, but complete resection is indicated because of the risk for progression. Chemotherapy may be useful in a subset of children at increased risk for recurrence/progression. Efforts to risk stratify children with type I PPB to optimize outcomes while reducing treatment-related side effects are underway.