Reconstructive Options in Genitourinary Rhabdomyosarcoma

Abstract

No AccessJournal of UrologyPediatric Urology1 Nov 1996Reconstructive Options in Genitourinary Rhabdomyosarcoma Barry P. Duel, W. Hardy Hendren, Stuart B. Bauer, James Mandell, Arnold Colodny, Craig A. Peters, Anthony Atala, and Alan B. Retik Barry P. DuelBarry P. Duel More articles by this author , W. Hardy HendrenW. Hardy Hendren More articles by this author , Stuart B. BauerStuart B. Bauer More articles by this author , James MandellJames Mandell More articles by this author , Arnold ColodnyArnold Colodny More articles by this author , Craig A. PetersCraig A. Peters More articles by this author , Anthony AtalaAnthony Atala More articles by this author , and Alan B. RetikAlan B. Retik More articles by this author View All Author Informationhttps://doi.org/10.1016/S0022-5347(01)65540-XAboutFull TextPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissionsReprints ShareFacebookLinked InTwitterEmail Abstract Purpose: We attempted to develop a rational and consistent scheme for surgical reconstruction in patients with genitourinary rhabdomyosarcoma. Materials and Methods: We reviewed the records of 35 patients with resectable genitourinary rhabdomyosarcoma treated from 1970 to 1993. Results: Primary sites included bladder in 11 cases, prostate in 13, vagina/uterus in 9 and pelvic tumors of uncertain origin in 2. A total of 33 patients underwent surgery, including partial and radical cystectomy in 17 (bowel conduit diversion in 10, continent urinary diversion in 6 and ureterosigmoidostomy in 1). Overall 30 of the 33 surgical patients are free of disease 4 months to 24 years after diagnosis. Conclusions: A nonrefluxing colon conduit is appropriate at cystectomy. Continent diversion fashioned from the original conduit may be planned as the patient achieves a durable disease-free status. References 1 : Bladder and prostatic tumors in the Intergroup Rhabdomyosarcoma Study: IRS-I: results of therapy. Cancer1982; 50: 1472. Google Scholar 2 : Genitourinary rhabdomyosarcoma in children. Cancer1989; 63: 1600. Google Scholar 3 : Sequelae of treatment in 109 patients followed for 5 to 15 years after diagnosis of sarcoma of the bladder and prostate. A report from the Intergroup Rhabdomyosarcoma Study Committee. Cancer1993; 71: 2387. Google Scholar 4 : The use of continent diversion in the management of rhabdomyosarcoma of the prostate in childhood. J. Urol.1992; 147: 1602. Abstract, Google Scholar 5 : Replacement of the bladder by the urethral Kock pouch: functional results, urodynamics and radiological features. J. Urol.1989; 141: 1111. Link, Google Scholar Division of Urology, Department of Surgery, Children's Hospital and Department of Surgery, Harvard Medical School, Boston, Massachusetts.© 1996 by American Urological Association, Inc.FiguresReferencesRelatedDetailsCited ByCastagnetti M, Angelini L, Alaggio R, Scarzello G, Bisogno G and Rigamonti W (2018) Oncologic Outcome and Urinary Function after Radical Cystectomy for Rhabdomyosarcoma in Children: Role of the Orthotopic Ileal Neobladder Based on 15-Year Experience at a Single CenterJournal of Urology, VOL. 191, NO. 6, (1850-1855), Online publication date: 1-Jun-2014.Rigamonti W, Iafrate M, Milani C, Capizzi A, Bisogno G, Carli M and Glazel G (2018) Orthotopic Continent Urinary Diversion After Radical Cystectomy in Pediatric Patients With Genitourinary RhabdomyosarcomaJournal of Urology, VOL. 175, NO. 3, (1092-1096), Online publication date: 1-Mar-2006.Ferrer F, Isakoff M and Koyle M (2018) Bladder/Prostate Rhabdomyosarcoma: Past, Present and FutureJournal of Urology, VOL. 176, NO. 4, (1283-1291), Online publication date: 1-Oct-2006.MERGUERIAN P, AGARWAL S, GREENBERG M, BAGLI D, KHOURY A and McLORIE G (2018) OUTCOME ANALYSIS OF RHABDOMYOSARCOMA OF THE LOWER URINARY TRACTJournal of Urology, VOL. 160, NO. 3 Part 2, (1191-1194), Online publication date: 1-Sep-1998. Volume 156Issue 5November 1996Page: 1798-1804 Advertisement Copyright & Permissions© 1996 by American Urological Association, Inc.MetricsAuthor Information Barry P. Duel More articles by this author W. Hardy Hendren More articles by this author Stuart B. Bauer More articles by this author James Mandell More articles by this author Arnold Colodny More articles by this author Craig A. Peters More articles by this author Anthony Atala More articles by this author Alan B. Retik More articles by this author Expand All Advertisement PDF DownloadLoading ...