Thoracic lymphangiomatosis.

Abstract

We report the case of a 33-year-old man with thoracic lymphangiomatosis. The patient had experienced a 17-year history of recurrent chylothoraces and worsening cor pulmonale. The neoplasm was composed of histologically benign lymphatic channels lined by endothelial cells containing factor VIII-related antigen by immunohistochemical staining. The neoplasm filled the chest cavity, thereby compressing the lungs and involving the pleura, mediastinum, and thoracic vertebrae. We contrast this case with previous reports of lymphangiomatosis.