Idebenone treatment in Friedreich patients: One-year-long randomized placebo-controlled trial

Effect of idebenone on cardiomyopathy in Friedreich's ataxia: a preliminary study

Pierre Rustin, Jürgen‐Christoph von Kleist-Retzow, Karine Chantrel-Groussard et al. · The Lancet · 1999 · 350 citations

Medicine, Neurology, Pharmacology +9

The yeast frataxin homolog Yfh1p plays a specific role in the maturation of cellular Fe/S proteins

Ulrich Mühlenhoff · Human Molecular Genetics · 2002 · 322 citations · Full text

Life Sciences, Genetics, Molecular Biology +17

Idebenone and reduced cardiac hypertrophy in Friedreich's ataxia

ANA HAUSSE · Heart · 2002 · 247 citations · Full text

Life Sciences, Cardiology, Pharmacology +13

Antioxidant treatment improves in vivo cardiac and skeletal muscle bioenergetics in patients with Friedreich's ataxia

Raffaele Lodi, Paul Hart, B. Rajagopalan et al. · Annals of Neurology · 2001 · 230 citations

Life Sciences, Biochemistry, Physiology +17

Cell death triggered by polyglutamine-expanded huntingtin in a neuronal cell line is associated with degradation of CREB-binding protein

Haibing Jiang · Human Molecular Genetics · 2003 · 186 citations

Life Sciences, Genetics, Neuroscience +17