Straatsma Syndrome: Should Visual Prognostic Factors Be Taken into Account? A Case Report

Abstract

Case 1 An 8-year-old girl was referred to our clinic with a 1-year history of blurred vision in the right eye (RE). Her family history was unremarkable. On examination, the patient's best-corrected visual acuity (BCVA) was 6/120 in the RE and 6/6 in the left eye (LE). Cycloplegic refraction was -3.00 diopters (D) in the RE and -0.25 D in the LE. Pupillary reflexes were equal and symmetric with no relative afferent pupillary defect. Cover-uncover and alternate cover tests were normal for both distance and near fixation. Bilateral slit-lamp examination and Goldmann applanation tonometry were unremarkable. Dilated fundus examination of the RE revealed 5 clock hours of MRNF along the superior arcade and 4 clock hours of MRNF along the inferior arcades with the macula spared, normal foveal reflex, and normal optic disc