Lumacaftor/ivacaftor improves liver cholesterol metabolism but does not influence hypocholesterolemia in patients with cystic fibrosis

Severity of cystic fibrosis in patients homozygous and heterozygous for ΔF508 mutation

H. Johansen, M. Nir, Claus Koch et al. · The Lancet · 1991 · 167 citations

Life Sciences, Genetics, Molecular Genetics +11

Effects of Lumacaftor–Ivacaftor Therapy on Cystic Fibrosis Transmembrane Conductance Regulator Function in Phe508del Homozygous Patients with Cystic Fibrosis

Simon Y. Graeber, Christian Dopfer, Lutz Naehrlich et al. · American Journal of Respiratory and Critical Care Medicine · 2018 · 117 citations

Medicine, Pharmacology, Pharmacotherapy +15

Altered cholesterol homeostasis in cultured and in vivo models of cystic fibrosis

Nicole M. White, Dechen Jiang, James D. Burgess et al. · American Journal of Physiology-Lung Cellular and Molecular Physiology · 2006 · 94 citations

Life Sciences, Biochemistry, Cell Biology +17

Hypocholesterolemia is an independent risk factor for depression disorder and suicide attempt in Northern Mexican population

Marcela Araceli Segoviano-Mendoza, Manuel Cárdenas-de la Cruz, José Salas-Pacheco et al. · BMC Psychiatry · 2018 · 86 citations · Full text

Medicine, Psychiatry, Adult Psychiatry +12

ESPGHAN and NASPGHAN Report on the Assessment of Exocrine Pancreatic Function and Pancreatitis in Children

Chris Taylor, Kathy Chen, Károly Horváth et al. · Journal of Pediatric Gastroenterology and Nutrition · 2015 · 77 citations

Medicine, Clinical Sciences, Pediatrics +14