PubMed · 2017 · 11 citations · 17 references
MedicineDermatologyPathologyDermatologic SurgeryDermatopathologyHistopathologyGranulomatous DermatosesGranulomatous InflammationCutaneous AutoimmunityGranulomatous LesionsGranulomatous Skin InflammationPyoderma GangrenosumVasculitis Pathogenesis
Granulomatosis with polyangitis, formerly known as Wegener's granulomatosis, is a multi-system vasculitis that has a variable clinical presentation. Although uncommon, cutaneous symptoms can be the initial presenting symptom of granulomatosis with polyangitis. We present an unusual case of pyoderma gangrenosum followed by a diagnosis of granulomatosis with polyangitis. We also provide a review of current literature on therapeutic options.
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Rituximab versus Cyclophosphamide for ANCA-Associated Vasculitis
John H. Stone, Peter A. Merkel, Robert Spiera et al. · New England Journal of Medicine · 2010 · 2.7K citations · Full text