<p>Brittle cornea syndrome: current perspectives</p>

Andrew Walkden, Emma Burkitt Wright, Leon Au

Clinical ophthalmology · 2019 · 33 citations · 33 references

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Abstract

Abstract: Brittle cornea syndrome (BCS) is a rare autosomal recessive connective tissue disorder characterised by severe corneal thinning, with the major ocular risk being spontaneous ocular perforation due to progressive stromal thinning and ectasia. It is a complex condition with limited treatment options. The purpose of this review is to highlight the difficulties associated with the condition and examine the available published evidence with regards to management. Keywords: brittle Cornea, spontaneous corneal perforation, corneal ectasia A Letter to the Editor has been published for this article A Response to Letter has been published for this article

References

33