Effects of Lumacaftor/Ivacaftor on physical activity and exercise tolerance in three adults with cystic fibrosis

The Anaerobic Threshold Measurement to Evaluate Exercise Performance

Karlman Wasserman · American Review of Respiratory Disease · 1984 · 415 citations

Life Sciences, Kinesiology, Physiology +17

Assessment of safety and efficacy of long-term treatment with combination lumacaftor and ivacaftor therapy in patients with cystic fibrosis homozygous for the F508del-CFTR mutation (PROGRESS): a phase 3, extension study

Michael W. Konstan, Edward F. McKone, Richard B. Moss et al. · The Lancet Respiratory Medicine · 2016 · 286 citations

Life Sciences, Genetics, Pharmacotherapy +15

Improvement in exercise duration, lung function and well-being in G551D-cystic fibrosis patients: a double-blind, placebo-controlled, randomized, cross-over study with ivacaftor treatment

Deirdre Edgeworth, D. Keating, Matthew J. Ellis et al. · Clinical Science · 2017 · 61 citations

Medicine, Physiology, Exercise Physiology +16

Relationship between pulmonary exacerbations and daily physical activity in adults with cystic fibrosis

Daniela Savi, Nicholas J. Simmonds, Marcello Di Paolo et al. · BMC Pulmonary Medicine · 2015 · 37 citations · Full text

Education, Health Behavior, Exercise Testing +13

Do responses to exercise training in cystic fibrosis depend on initial fitness level?

Wolfgang Gruber, David M. Orenstein, K.-M. Braumann · European Respiratory Journal · 2011 · 26 citations · Full text

Education, Physiology, Rehabilitation Medicine +17