Transplantation Direct · 2019 · 12 citations · 3 references
MedicinePathologyRadiologyHepatologyTransplant SurgeryTumor PathologyBiliary Tract DiseaseHepatic PathologyHepatobiliary DiseaseHepatobiliary PathologyLiver DiseaseLiver TransplantationBiliary HamartomaHepatic Tumor ImagingLiver Transplantation Management
Von Meyenburg complexes, or multiple biliary hamartomas, are often asymptomatic lesions incidentally discovered during abdominal or hepatic imaging. The presentation of clinically significant Von Meyenburg complexes ranges from cholestasis and self-limited episodes of cholangitis to malignant degeneration into cholangiocarcinoma. In cases of persistent or recurrent cholangitis, treatment is a significant challenge. Definitive source control with liver transplantation, as in other cases of cholestatic liver disease, may be necessary.
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Imaging findings of biliary hamartomas
Rongqin Zheng · World Journal of Gastroenterology · 2005 · 122 citations · Full text
The clinical presentation of Von Meyenburg complexes.
Emmanouil Sinakos, Lavrentios Papalavrentios, Danai Chourmouzi et al. · PubMed · 2011 · 36 citations