Primary Cerebral Arterial Occlusive Disease in Children

Abstract

Cerebral angiography was performed in the cases of 3 children with multiple neurofibromatosis, 2 with encephalotrigeminal angiomatosis, and 2 with tuberous sclerosis. All children had a distal branch occlusion with or without other vascular lesions. Tortuosity, segmental ectasia, and stenosis of the cerebral vessels were encountered in this series, but not in the children described in Part 1. The lesions, however, did not conform to a pattern.