Fatal Nontraumatic Splenic Rupture in Hemophilia and the Kasabach-Merritt Syndrome

Abstract

Fatal nontraumatic splenic rupture is documented in two patients, one with classical hemophilia and the other with the Kasabach-Merritt syndrome. Splenic rupture was due to multiple hemangioma-like lesions in both patients. These lesions apparently were acquired, possibly as a result of infection an