PubMed · 1976 · 17 citations · 0 references
MedicinePediatricsRadiologyDiagnostic RadiologyPediatric RadiologyThoracic RadiologyChest RadiologyCongenital Lung MalformationsCongenital Thoracic AnomaliesVascular AnomaliesVascular MalformationsBronchopulmonary SequestrationPediatric Vascular MalformationsPulmonary Artery AnomaliesPulmonary SequestrationScimitar Syndrome
Bronchopulmonary sequestration (BPS), a congenital malformation that usually presents as a chest mass in childhood, may be identified by its characteristic primary derivation of pulmonary blood supply from the systemic circulation. Five children with BPS were evaluated by radionuclide angiography from 1970 to 1974. In each instance the systemic origin of the vascular supply was correctly indicated. In those lesions where the artery originates below the hemidiaphragm, the aberrant source, when identified as such, provides a characteristic radionuclide appearance of BPS. The scimitar syndrome may be indistinguishable from BPS with this technique.