Intravascular malignant lymphoma ("malignant angioendotheliomatosis") mimicking primary angiitis of the central nervous system.

Abstract

Malignant angioendotheliomatosis is characterized by the plugging of central nervous system blood vessels with large mononuclear cells, thus mimicking primary angiitis of the central nervous system. When autoantibodies are present, it can mimic connective tissue disease. Treatment of malignant angioendotheliomatosis with cytoxan may prolong survival.