PubMed · 1983 · 12 citations · 0 references
MedicineCardiologyCardiovascular GeneticsClinical CardiologyElectrophysiologyInherited CardiomyopathiesMendelian Cardiovascular DisordersMuscle DisordersMuscle PathologyMuscular DystrophyDuchenne Muscular Dystrophy InheritanceEchocardiographic HemodynamicsEchocardiographic InterpretationMuscular Dystrophy GeneticsMuscular Dystrophy PathophysiologyMyocardial AnatomyMyocardial ArchitectureMyocardial Degeneration
The electro-, phonomechano- and echocardiographic manifestations observed in a family with documented X-linked Becker-type muscular dystrophy (BMD) are described. Important myocardial dystrophic lesions may occur in young patients with BMD. They are associated with typical electrocardiological findings which were described as a distinctive pattern in Duchenne-type muscular dystrophy. Myocardial involvement is seldom observed in heterozygotes for BMD.