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Duodenal somatostatinoma with congenital pseudoarthrosis.
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1991
Year
Clinical FindingVon RecklinghausenSurgical PathologyHistopathologyPathologyDuodenal SomatostatinomaDermatologySclerodermaMedicineCongenital PseudoarthrosisPathologic LesionRheumatoid ArthritisConnective Tissue Disease
We describe a previously unreported association between somatostatinoma and congenital pseudoarthrosis. Because pseudoarthrosis is part of von Recklinghausen's disease, in turn with an association with somatostatinoma, we speculate on a link between pseudoarthrosis and somatostatinoma.