Kidney Transplantation in Fanconi Syndrome

Abstract

KIDNEY transplantation in children and adolescents with end-stage renal disease will provide information regarding the possibility of recurrence in the transplanted kidney of diseases unique to children. This report presents the contrasting post-transplant courses of two patients with the Fanconi syndrome, one with the idiopathic variety and the other with cystinosis.Case ReportsCase 1. A 14-year-old boy was found to have idiopathic Fanconi syndrome at the age of 5. Progressive renal insufficiency ensued, requiring hemodialysis in 1968. Ophthalmologic and bone-marrow examinations were negative for cystine, as were the kidneys after nephrectomy.In May, 1969, he received a maternal renal . . .