American Journal of Clinical Pathology · 1993 · 11 citations · 0 references
MedicineHematologyPediatricsHematopathologyPediatric HematologyTransfusion MedicineHematologic DisordersHemostatic DisordersPlatelet DisordersPlatelet FunctionPlatelet PhysiologyPlatelet TransfusionAutologous Platelet ConcentratesPediatric ThrombocytopeniaPlatelet Disorder ManagementPlatelet Transfusion In NeonatesPlatelet Transfusion In ThrombocytopeniaPlatelet Transfusion Therapy
The Kasabach-Merritt Syndrome describes thrombocytopenia occurring in patients with giant hemangiomata. The resultant thrombocytopenia may be profound and occasionally even life-threatening. An 11-month-old infant with prolonged thrombocytopenia whose course was complicated by recurrent hemorrhaging requiring intense platelet transfusions is reported. During her 19-month hospitalization she received 6,622 platelet concentrates. This represents the most extensive platelet support ever given to an infant with this syndrome.