Pulmonary Artery Agenesis and Lung Hypoplasia

Abstract

Unilateral pulmonary artery agenesis with lung hypoplasia is very rare and only a few cases have been reported in the literature. Some patients with hypoplasia may suffer from recurrent hemoptysis dyspnea, and lung infections. Other patients are asymptomatic. Chest X-Ray reveal a reduction in the volume of hemithorax, an elevation in the diaphragm, reduced intercostals spaces and mediastinal shift in the affected side. We present a 15 year old male patient who complained of shortness of breath and chest pain.