Journal of Cardiovascular Medicine · 2007 · 10 citations · 8 references
MedicineCardiologyInternal MedicineCardiovascular GeneticsClinical CardiologyElectrophysiologyAtrial FibrillationCardiac ArrhythmiasElectrocardiogram InterpretationElectrocardiographyInherited Arrhythmia SyndromesIntracardiac ElectrophysiologyAmiodarone TherapyAtrial Fibrillation SyndromesFlecainide TherapyFollow-up DurationImplantable Cardioverter Defibrillators
We report the case of a patient with genetically confirmed Brugada syndrome who presented with ST-segment elevation in the right precordial and inferior leads. The presenting arrhythmia was atrial fibrillation, which degenerated into ventricular fibrillation during intravenous amiodarone. A flecainide test was markedly positive. Four appropriate cardioverter-defibrillator discharges occurred during a two-year follow-up period after implantation of the device.
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Natural History of Brugada Syndrome
Silvia G. Priori, Carlo Napolitano, Maurizio Gasparini et al. · Circulation · 2002 · 1K citations
Medicine, Cardiology, Genetics +17
Josép Brugada, Ramón Brugada, Charles Antzelevitch et al. · Circulation · 2002 · 628 citations · Full text