Oman Medical Journal · 2014 · 14 citations · 9 references
MedicineNeurologyNeuroscienceDiagnostic ImagingDiagnostic RadiologyNeurodegenerationBrain ImagingEncephalitisNeurodegenerative Disease ImagingNeurodegenerative DisordersNeurologic ImagingNeurological AssessmentDifferential Diagnostic CriteriaEncephalitis DiagnosisEncephalitis Differential DiagnosisInflammatory Neurologic DisordersNeurodegenerative Disease CasesNeurodegenerative Disease MechanismsNeurological DeteriorationSeizures
Rasmussen encephalitis is an extremely rare chronic inflammatory neurodegenerative disease affecting a single cerebral hemisphere, causing progressive neurological deterioration and intractable seizures. Imaging plays an important role in diagnosis by demonstrating focal or unihemispheric involvement and excluding other possible causes. Here, we report a case of Rasmussen encephalitis with an update on recent diagnostic criteria and emphasis on differential diagnoses which can be excluded on imaging.
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Autoantibodies to Glutamate Receptor GluR3 in Rasmussen's Encephalitis
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Theodore P. Rasmussen, Donald Lloyd-Smith · Neurology · 1958 · 544 citations · Full text
Medicine, Neurology, Sports Medicine +16
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Christian G. Bien, Guido Widman, Horst Urbach et al. · Brain · 2002 · 282 citations · Full text
Medicine, Neurology, Neuroscience +16
Diagnosis and staging of Rasmussen’s encephalitis by serial MRI and histopathology
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Medicine, Neurology, Neuroscience +17