A case of 75-year old survivor of unrepaired tetralogy of Fallot and quadricuspid aortic valve

Abstract

In tetralogy of Fallot (TOF), the most common form of cyanotic congenital heart disease, only a few patients reach adulthood without surgical correction. We present the case of a man with TOF who survived until the age of 75 years without surgical intervention and had a very unusual combination of TOF and quadricuspid aortic valve (QAV). QAV, complicated by aortic regurgitation, is an uncommon finding in TOF patients. The hemodynamic consequences for both the right and left ventricles are significant. This case provides a rare insight into the late outcome of an elderly patient with uncorrected TOF.