Stargardt's hereditary progressive macular degeneration.

Abstract

In a series of three papers, Stargardt ( 1909,I93, I9I6) described with precision and thoroughness a form of hereditary macular degeneration which has become known as Stargardt's disease. The purposes of the present paper are to review Stargardt's original observations, to argue that Stargardt's disease and fundus flavimaculatus with atrophic macular degeneration are identical, and to present a series of patients studied by fluorescein angiography consistent with the hypothesis that a late secondary or disuse atrophy of the choriocapillaris occurs in Stargardt's disease.