European Respiratory Society guidelines for the diagnosis and management of lymphangioleiomyomatosis

Abstract

Review Panel of the ERS LAM Task Force L ymphangioleiomyomatosis (LAM) is a rare lung disease, which occurs sporadically or in association with the genetic disease tuberous sclerosis complex (TSC) Sporadic LAM affects ,1 in 400,000 adult females; in TSC, LAM occurs in 30-40% of adult females