Neonatal Tuberous Sclerosis with Cardiac Rhabdomyomas Presenting as Fetal Supraventricular Tachycardia.

Abstract

A case of fetal tuberous sclerosis with multiple intracardiac rhabdomyomas exhibited persistent supraventricular tachycardia. The tachycardia was terminated by the use of cardiac version. The largest tumor almost occluded the right ventricular inlet portion. The obstruction was relieved after surgical removal of the largest tumor. No arrhythmia was noted after 3 months of follow-up.