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SARCOID ARTHROPATHY IN CYSTIC FIBROSIS
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1989
Year
RheumatologyFibrosisPulmonary PathologyVasculitisAutoimmune DiseaseHistopathology8-Year-old BoyPathologyPaediatric RheumatologyDermatologyChronic PolyarthritisMedicineConnective Tissue Disease
An 8-year-old boy with cystic fibrosis presented with a chronic polyarthritis. Histological examination of the synovium demonstrated multiple non-caseating granulomata. A systematic search for sarcoidosis revealed characteristic ophthalmic abnormalities and an elevated serum level of angiotensin converting enzyme. An association between cystic fibrosis and sarcoidosis is likely.