Electrocardiographic and Clinical Characteristics of Idiopathic Restrictive Cardiomyopathy in Children

Abstract

Obliquely elevated ST-T segments and the late peak T wave on ECG are characteristic, and reflect the restrictive physiology, which may indicate abnormalities of repolarization of ventricular muscle. The mode of death was either heart failure from pulmonary hypertension or sudden death from presumed ventricular arrhythmia.