Concepedia

Publication | Closed Access

Management of acute metabolic decompensation in maple syrup urine disease: A multi-center study

DOI

36

Citations

0

References

1999

Year

Makoto Yoshino, Kikumaro Aoki, Hideki Akeda, Kazuko Hashimoto, Tetsuo Ikeda, Fumio Inoue, Michinori Ito, Masahiko Kawamura, Yoshinori Kohno, Yasutoshi Koga,
Pediatrics International

Abstract

Therapeutic goals to improve neurological outcome are to shorten the duration of the altered level of consciousness, and to minimize the peak plasma leucine level as much as possible.