Publication | Open Access
Muscular false tendons, aberrant left ventricular papillary musculature, and severe electrocardiographic repolarisation abnormalities: a new syndrome.
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1994
Year
Cardiac MuscleHeart FailureNormal Exercise CapacityCongenital Heart AnomalyStructural Heart DiseaseVentricular Papillary MusculatureElectrophysiological EvaluationPapillary MusclesCongenital Heart DefectNew SyndromeCardiologyRadiologyCardiovascular ImagingCardiomyopathyAge 18-39Muscular False TendonsCardiac PathologyMedicineCardiovascular Genetics
Three patients (age 18-39 years; two men) with normal exercise capacity, normal left ventricular function, large muscular false tendons within the left ventricle, and anomalously placed papillary muscles associated with giant T wave inversion on the electrocardiogram are described. The absence of adverse cardiovascular events at long-term follow up (mean 13 years) indicates that this is a benign unrecognised syndrome.