British Journal of Dermatology · 1992 · 26 citations · 3 references
Life SciencesBiochemistryPediatricsClinical BiochemistryExcretionTransfusion MedicineEnzyme DeficienciesPediatric TransfusionUrinary ExcretionRed Blood Cell Enzyme Deficiencies
A case is reported of a 15-year-old boy with prolidase deficiency and marked urinary excretion of the iminodipeptide gly-pro. Prolidase activity of erythrocytes against substrate glycyl-proline was deficient, but after blood transfusions this was increased to 15.7% of donor activity and declined to 12% and 3.4% of normal activity after 8 and 45 days, respectively. Urinary iminodipeptide levels following transfusion remained unaltered.
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P. S Harper · Journal of Medical Genetics · 1987 · 581 citations · Full text