GROWTH OF MANDIBLE IN INFANTS WITH MICROGNATHIA<subtitle>Clinical Implications</subtitle>

Abstract

SINCE Pierre Robin first described the syndrome of hypoplasia of the mandible, cleft palate, glossoptosis, inspiratory retraction of the sternum, cyanosis, and malnutrition which has come to bear his name,* numerous reports of cases have appeared in the literature. The fatal termination of some cases is a testimony of the serious nature of the syndrome. Although a variety of mechanical and surgical therapeutic procedures have been suggested,† a rationale for the proper management of individual patients has not been adequately presented. It is the purpose of this communication to present observations from the serial studies of patients with this disorder, upon which a physiologic approach to management may be based. It is generally agreed that the pathophysiologic events in this syndrome are as follows: the receding chin fails to support the tongue in its normal forward relationship and hence fosters the glossoptosis. The retroposed tongue impinges against the posterior wall