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Antenatal Ultrasound Findings in a Case of Uhl's Anomaly
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1988
Year
Antenatal Ultrasound FindingsMedical UltrasoundTotal AbsenceRight Ventricular MyocardiumPediatricsDiagnosisCongenital Heart DefectPrenatal DiagnosisSevere Congenital UhlUltrasoundCongenital Heart AnomalyMedicineCardiology
A case of severe congenital Uhl's anomaly is described. Uhl's anomaly is a rare disorder characterized by near total absence of the right ventricular myocardium. Antenatal ultrasound and echocardiographic findings are presented and the differential diagnosis is discussed.