A tri-linear pattern of scleroderma ‘en coup de sabre’ following Blaschko's lines

Abstract

Linear scleroderma 'en coup de sabre' is characterized by atrophy and furrowing of the skin of the frontoparietal region. In most cases it occurs as a single, paramedian line that may be associated with hypoplasia of underlying structures and hemiatrophy of the face. Rarely, lesions form two lines, either both on the same side or bilaterally. We describe an 18-year-old male with an unusual tri-linear pattern of scleroderma 'en coup de sabre' following Blaschko's lines.