Concepedia

Morphological alterations and induction of oxidative stress in glial cells caused by the branched-chain α-keto acids accumulating in maple syrup urine disease

Cláudia Funchal, Alexandra Latini, Maria C. Jacques-Silva, André Quincozes dos Santos, Luciane Buzin, Carmem Gottfried, Moaçir Wajner, Regina Pessoa‐Pureur

Neurochemistry International · 2006 · 65 citations · 51 references

Concepts

BiochemistryMorphological AlterationsLipid PeroxidationPathologyMolecular NutritionMetabolismMetabolic SignalingMedicineCell BiologyBranched-chain α-Keto AcidsOxidative Stress

References

51

Cleavage of Structural Proteins during the Assembly of the Head of Bacteriophage T4

Ulrich K. Laemmli · Nature · 1970 · 251K citations

Protein Assembly, Natural Sciences, Structural Proteins +8

[13] Catalase in vitro

H. Aebi · Methods in enzymology on CD-ROM/Methods in enzymology · 1984 · 24.5K citations

Biotransformation, Biochemistry, Natural Sciences +3

Free radicals in biology and medicine

General Pharmacology The Vascular System · 1991 · 17.2K citations

Biochemistry, Medicine, Radical (Chemistry) +8

The Metabolic Basis of Inherited Disease.

Annals of Internal Medicine · 1988 · 7.8K citations

Metabolic Syndrome, Energy Metabolism, Disease Mechanism +12

The metabolic and molecular bases of inherited disease

Ying-Tsong Chen · Medical Entomology and Zoology · 2001 · 6.9K citations

Disease Mechanism, Genetic Disorder, Genetics +6