Fatal heart failure associated with CoQ10 and multiple OXPHOS deficiency in a child with propionic acidemia

A Rapid and Sensitive Method for the Quantitation of Microgram Quantities of Protein Utilizing the Principle of Protein-Dye Binding

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A rapid and sensitive method for the quantitation of microgram quantities of protein utilizing the principle of protein-dye binding

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On the mechanism of action of the antifungal agent propionate

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Secondary mitochondrial dysfunction in propionic aciduria: a pathogenic role for endogenous mitochondrial toxins

Marina A. Schwab, Sven W. Sauer, Jürgen G. Okun et al. · Biochemical Journal · 2006 · 189 citations · Full text

Multiple OXPHOS Deficiency in the Liver, Kidney, Heart, and Skeletal Muscle of Patients With Methylmalonic Aciduria and Propionic Aciduria

Yves de Keyzer, Vassili Valayannopoulos, Jean‐François Benoist et al. · Pediatric Research · 2009 · 166 citations · Full text

Urology, Multiple Oxphos Deficiency, Methylmalonic Aciduria +8