Journal of Pediatric Hematology/Oncology · 1993 · 27 citations · 0 references
MedicineOncologyPathologyNeoplasiaPediatric OncologyTumor PathologyPediatric TumorsPediatric Urologic OncologyRenal NeoplasmsWilms TumorGross Pathologic ExaminationHistologic RemissionLumbosacral DiseaseLumbosacral LipomaMalignant Soft Tissue NeoplasmsPathologic ClassificationPediatric Soft Tissue TumorsWilms Tumor Surgery
True extrarenal Wilms' tumor is a rare malignant neoplasm most frequently presenting in the retroperitoneal or inguinal regions. We report an unusual subcutaneous lumbosacral (LS) region extrarenal Wilms' tumor without associated teratomatous tumor elements or associated neural tube defect in a 2 1/2-year-old girl. Pathologic review revealed features of true extrarenal Wilms' tumor, and the patient remains in complete remission following surgery and combination chemotherapy. This report illustrates the importance of early surgical intervention and pathologic examination of similar soft tissue masses in children.