Primary Ewing’s Sarcoma of the Occipital Bone Presenting as Hydrocephalus and Blindness

Abstract

Ewing’s sarcoma was first described by James Ewing in 1921. It is most often seen in the long bones of the lower limbs and pelvis, and typically affects children and young adults [1, 2] . Metastatic Ewing’s sarcoma to skull bones is seen frequently, but primary Ewing’s sarcoma of the skull bone is rarely encountered in neurosurgical practice [1, 2] . These patients usually present with headache due to a local mass effect, but presentation with obstructive hydrocephalus is distinctly rare [3] . The present case is the first in the existing medical literature of Ewing’s sarcoma of skull bone presenting as obstructive hydrocephalus and blindness.