A previously undescribed hereditary hair anomaly (pseudo-monilethrix)

Abstract

A new term ‘pseudo‐monilethrix’ is suggested for an unusual form of ‘beaded’ hair, found in many members of a large Caucasoid family. The abnormality bears a resemblance to classical monilethrix but is not the same condition. Other associated anomalies are formes frustes of pili torti and trichorrhexis nodosa. These disorders are traced through four generations and appear to have been inherited as an autosomal dominant trait. The clinical features and prognosis are discussed and the results of the examination of hairs under the light and scanning electron‐microscopes are recorded.