PULMONARY ATRESIA WITH INTACT VENTRICULAR SEPTUM

Abstract

Although congenital pulmonary atresia with an intact ventricular septum is an uncommon malformation, its recognition is important because the results of surgical treatment may be favour- able in some cases. Functionally, this entity belongs to a group of congenital malformations each having obstruction to pulmonary flow. This group includes severe pulmonary stenosis, tricuspid atresia, pulmonary atresia with a ventricular septal defect, and the origin of the aorta and pulmonary trunk from the right ventricle with severe pulmonarystenosis.