Longterm Survival Among Patients with Scleroderma-associated Pulmonary Arterial Hypertension Treated with Intravenous Epoprostenol

David B. Badesch, Michael D. McGoon, Robin J. Barst, Victor F. Tapson, Lewis J. Rubin, Fredrick M. Wigley, Kenneth M. Kral, Ibrahim Raphiou, Glenn Crater

The Journal of Rheumatology · 2009 · 85 citations · 18 references

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Abstract

This study reports longterm survival rates for patients with scleroderma-associated PAH treated with i.v. epoprostenol. Although comparisons to historical data should be made with caution, this study reports a better survival outcome than natural history data on patients with scleroderma-associated PAH.

References

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