Dermatology · 2009 · 31 citations · 0 references
MedicineNephrologyPathologyAnatomic PathologyHistopathologyRenal PathologyCongenital Renal AnomaliesMesenchymal TumorsNephrotic SyndromeSoft Tissue PathologyVascular MalformationsBenign Soft Tissue NeoplasmsCongenital Nephrotic AnomaliesCongenital Soft Tissue DefectsEmbryonic PhysiologyMesenteric Pathology
Melorheostosis is a benign, rare, congenital disorder of hyperostosis of one or more bones. Associated soft tissue abnormalities are often observed. A case of melorheostosis with minimal change nephrotic syndrome, mesenteric fibromatosis and capillary haemangiomas is reported. A congenital mesenchymal defect occurring early in embryonic life is suggested.