Melorheostosis with Associated Minimal Change Nephrotic Syndrome, Mesenteric Fibromatosis and Capillary Haemangiomas

Douglas J. Roger, J.-M. Bonnetblanc, C. Leroux‐Robert

Dermatology · 2009 · 31 citations · 0 references

Concepts

Abstract

Melorheostosis is a benign, rare, congenital disorder of hyperostosis of one or more bones. Associated soft tissue abnormalities are often observed. A case of melorheostosis with minimal change nephrotic syndrome, mesenteric fibromatosis and capillary haemangiomas is reported. A congenital mesenchymal defect occurring early in embryonic life is suggested.