Possible Bradycardic Mode of Death and Successful Pacemaker Treatment in a Large Family with Features of Long QT Syndrome Type 3 and Brugada Syndrome - Concepedia

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Possible Bradycardic Mode of Death and Successful Pacemaker Treatment in a Large Family with Features of Long QT Syndrome Type 3 and Brugada Syndrome

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References

2001

Year

Maarten P. van den Berg, Arthur A.M. Wilde, J. W. Viersma, Jan Brouwer, J. Haaksma, Annemieke H. van der Hout, Irene Stolte‐Dijkstra, Connie R. Bezzina, Irene M. van Langen, Gertie C. M. Beaufort‐Krol,

Journal of Cardiovascular Electrophysiology

Abstract

This family with a high incidence of nocturnal sudden death is characterized by bradycardia-dependent QT prolongation, intrinsic sinus node dysfunction, and generalized conduction abnormalities. There is a striking absence of complex ventricular ectopy, and pacemaker implantation was effective in preventing sudden death. These findings raise the possibility of a bradycardic rather than tachycardic mode of death.