Progressive Familial Intrahepatic Cholestasis: Partial Biliary Diversion Normalizes Serum Lipids and Improves Growth in Noncirrhotic Patients

Abstract

This report shows an excellent result of DIV in noncirrhotic PFIC patients and compares favorably with other reports. All patients experienced complete remission, including normalization of synthetic liver function and lipid metabolism. For the first time we have shown that DIV can also be associated with an accelerated growth in these patients.