Dandy-Walker Malformation and Associated Cardiac Anomalies

Abstract

2 patients with Dandy-Walker malformations (DWM) and cardiac anomalies are presented. The types of cardiac defects with septal involvement are suggestive of an early embryonic abnormality occurring before 6 weeks' gestational age. This correlates with the postulated timing of the development of the DWM and suggests a complex developmental anomaly. Awareness of the associated systemic and central nervous system anomalies in patients with the DWM in regard to management and prognosis is emphasized.