Concepedia

Long-term data from the Familial Amyloidotic Polyneuropathy World Transplant Registry (FAPWTR)

H Wilczek, Markus Larsson, B.-G. Ericzon

Amyloid · 2011 · 96 citations · 8 references

DOI

Concepts

Abstract

Abstract: Familial amyloidotic polyneuropathy (FAP) is a fatal systemic disease, caused by an amyloidogenic transthyretin (TTR) variant. Orthotopic liver transplantation (OLT) eliminates the main s...

References

8

Clinical improvement and amyloid regression after liver transplantation in hereditary transthyretin amyloidosis

Gösta Holmgren, Lars Steen, Ole B. Suhr et al. · The Lancet · 1993 · 581 citations

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Biochemical effect of liver transplantation in two Swedish patients with familial amyloidotic polyneuropathy (FAP‐met<sup>30</sup>)

Gösta Holmgren, Lars Steen, Jan Ekstedt et al. · Clinical Genetics · 1991 · 398 citations

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PROGRESSIVE CARDIAC AMYLOIDOSIS FOLLOWING LIVER TRANSPLANTATION FOR FAMILIAL AMYLOID POLYNEUROPATHY

Arie J. Stangou, Philip N. Hawkins, Nigel Heaton et al. · Transplantation · 1998 · 210 citations

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Malnutrition and gastrointestinal dysfunction as prognostic factors for survival in familial amyloidotic polyneuropathy

Ole B. Suhr, Anna Danielsson, Gösta Holmgren et al. · Journal of Internal Medicine · 1994 · 209 citations

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Cardiac Amyloid in Patients with Familial Amyloid Polyneuropathy Consists of Abundant Wild-Type Transthyretin

Masahide Yazaki, Takahiko Tokuda, Akihiro Nakamura et al. · Biochemical and Biophysical Research Communications · 2000 · 166 citations

, , +13