Fatal haemolytic-uraemic syndrome in two sibs.

Abstract

The first clear account of this syndrome was published by Since then some 200 cases have been reported from all parts of the world (Piel and The syndrome is characterized by non-immune, Coombs negative, haemolytic anaemia, with bizarre red cells, variable thrombocytopenia, and acute renal failure. At necropsy the main findings are necrotizing glomerular lesions with fibrinous capillary thromboses.