Journal of Radiology Case Reports · 2014 · 17 citations · 13 references
Life SciencesNeurologyPathologyAutoimmunityNeuroimmunologyNeuropathologyAutoantigensAutoimmune DiseasesAutoimmune Neurological DisordersEncephalitisViral InfectionsEncephalitis DiagnosisEncephalitis Differential DiagnosisEncephalitis PathogenesisImmune-mediated EncephalitisOvarian TeratomaViral EncephalitisYoung Women
We report an interesting case of a 19 year old female with findings on MRI suggestive of viral encephalitis. An extensive workup was negative for infectious causes and she was subsequently diagnosed with anti-NMDA encephalitis. Anti-NMDA encephalitis is a highly lethal but treatable form of autoimmune encephalitis that has recently been characterized. It is frequently found in young women and associated with an underlying teratoma. Although rare, this diagnosis should be considered in young females for whom a rapid onset of encephalitis cannot be explained by more common causes.
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Anti-NMDA-receptor encephalitis: case series and analysis of the effects of antibodies
Josep Dalmau, Amy J. Gleichman, Ethan G. Hughes et al. · The Lancet Neurology · 2008 · 3.5K citations · Full text
Julia Granerød, Helen E. Ambrose, Nicholas Davies et al. · The Lancet Infectious Diseases · 2010 · 1.4K citations · Full text
Cellular and Synaptic Mechanisms of Anti-NMDA Receptor Encephalitis
Ethan G. Hughes, Xiaoyu Peng, Amy J. Gleichman et al. · Journal of Neuroscience · 2010 · 1.1K citations · Full text