Sacral Arachnoid Cyst Associated with Marfan Syndrome

Abstract

A 42-year-old man was admitted to Keiaido Hospital for sacral pain and dysesthesia in the segmental area S2 of the right lower extremity. He had been operated on for bilateral ectopia lentis. His uncle became blind by ectopia lentis and had undergone surgery for an aortic aneurysm. Multidetecter-low CT (MDCT) demonstrated the dilated sinuses of Valsalva (Fig. A diagnosis of Marfan syndrome was made. Further, lumbosacral magnetic resonance imaging (MRI) demonstrated a cystic lesion at the right S2 level (Fig. Communication with the subarachnoid space was revealed on computed tomography (CT)-myelography scan (Fig. A laminectomy of the sacrum was performed because S2 radiculopathy due to a sacral arachnoid cyst was suspected. A dark blue, cystic mass arose from the S3 root sheath and compressed the S2 root (Fig. The cyst was totally removed. Histopathological examination of the cyst wall revealed the features of a type I arachnoid cyst (Fig.