Riga‐Fede Disease Associated with Postanoxic Encephalopathy and Trisomy 21: A Proposed Classification

Abstract

We present a new instance of Riga-Fede disease in a 2-year-old boy with Down syndrome and postanoxic encephalopathy. We propose a classification of the disease, as either "precocious," associated with natal or neonatal teeth or "late-onset," associated with neurologic disease.